Complications following the Kasai procedure include recurrent cholangitis, pruritus, growth failure, hypersplenism, and portal hypertension with variceal bleeding. If the surgeon confirms the diagnosis of biliary atresia, a Kasai Procedure (hepato-portoenterostomy) is performed to reconstruct the bile ducts and restore bile flow. During a Kasai portoenterostomy, your child's surgeon removes the damaged bile ducts and connects the liver to the intestine. Anastomotic stenosis, recurrent cholangitis, progressive pathology with the loss of intrahepatic ducts contributes to the long-term failure of Kasai procedure. 153 patients receiving open KPE treated at a single center between 1994 and 2014 were analysed retrospectively regarding short-term complications … Accessing and dilating strictures at the Kasai site is a major challenge, remembering that the original sur-gery was not a choledocho-jejunal anastomosis but instead Kasai procedure, a hepatoportoenterostomy(HPE) as an attempt to restore bile flow from the liver to the proximal small bowel, has been shown to improve survival in BA patients. If biliary atresia appears to be the cause of jaundice, surgery to examine the bile ducts is performed. or at the Kasai portoenterostomy and the presence of obstructive intraductal gallstones. Following the surgery, your child may stay in the hospital between seven and 10 days. Please use one of the following formats to cite this article in your essay, paper or report: APA. Biliary atresia is a rare neonatal disease of unknown etiology, where obstruction of the biliary tree causes severe cholestasis, leading to biliary cirrhosis and death in the first years of life, if the condition is left untreated. Wilson, Damien Jonas. Some complications of biliary atresia can be treated temporarily with medications and special diets; liquid vitamin supplements can be given orally to help lessen deficiencies. Optimal approaches to the management of these biliary complications have not been defined. Kasai Procedure. Your child's healthcare provider will discuss which surgery would be a good choice for your child. Without surgery, biliary atresia can be fatal. (2019, February 26). This surgery connects the bile drainage from the liver directly to the intestinal tract. Most babies who clear jaundice after a Kasai procedure do so in two to three months after surgery. Following portoenterostomy, children with biliary atresia can develop acute and chronic complications. Medical treatment options are summarized in Table II. Although Kasai's hepatoportoenterostomy (KPE) is the well-established first-line therapy, little is known about its surgical complications. Atrésie biliaire et procédure de Kasai. This allows bile to drain directly from the small bile ducts at the edge of your child's liver straight into her intestine. The Kasai procedure is most successful in babies younger than 3-months-old, so early diagnosis is important. Two types of surgery are used to treat this condition. Kasai procedure. Complications. If the Kasai procedure is not successful, the only other option is a liver transplant. However, a suitable donor organ must be found quickly, before damage to … It is not unusual for liver function tests to remain abnormal even if the jaundice completely clears. Many BA survivals who had undergone Kasai HPE will have slowly progressive liverdisease and the majority of patients will ultimately require liver transplantation. Even if the jaundice clears after a Kasai operation some children will develop complications due to liver damage.